glutaric aciduria in children 6 months–10 years.

GEL, protein equivalent (essential and non-essential amino

acids except lysine, and low tryptophan) 10 g, carbohydrate

10.3 g, fat trace, energy 339 kJ (81 kcal)/24 g, with vitamins,

minerals, and trace elements. To flavour unflavoured products,

see FlavourPac p. 1575.

GA gel oral powder 24g sachets (Vitaflo International Ltd)

30 sachet (ACBS) . NHS indicative price = £233.35

GA1 Anamix ® Infant

▶ Nutritional supplement for the dietary management of proven

glutaric aciduria (type 1) in children from birth to 3 years.

POWDER, protein equivalent (essential and non-essential amino

acids except lysine, and low tryptophan) 13.1 g, carbohydrate

49.5 g, fat 23 g, fibre 5.3 g, energy 1915 kJ (457 kcal)/100 g, with

vitamins, minerals, and trace elements; standard dilution (15%)

provides protein equivalent 2 g, carbohydrate 7.4 g, fat 3.5 g,

fibre 800 mg, energy 287 kJ (69 kcal)/100 mL.

GA1 Anamix Infant powder (Nutricia Ltd)

400 gram (ACBS) . NHS indicative price = £42.17

XLYS, TRY Glutaridon ®

▶ Nutritional supplement for the dietary management of type 1

glutaric aciduria in children and adults; requires additional

source of vitamins, minerals, and trace elements.

POWDER, protein equivalent (essential and non-essential amino

acids except lysine and tryptophan) 79 g, carbohydrate 4 g,

energy 1411 kJ (332 kcal)/100 g. To flavour unflavoured

products, see Modjul Flavour System p. 1576.

XLYS TRY Glutaridon powder (Nutricia Ltd)

500 gram (ACBS) . NHS indicative price = £201.74

Glycogen storage disease

Corn flour and corn starch

▶ For glycogen storage disease

Glycosade ®

▶ A nutritional supplement for use in the dietary management of

glycogen storage disease and other metabolic conditions where

a constant supply of glucose is essential. Not suitable for use in

children under 2 years.

POWDER, protein 200 mg, carbohydrate (maize starch) 47.6 g,

fat 100 mg, fibre less than 600 mg, energy 803 kJ (192 kcal)/60 g.

Glycosade oral powder 60g sachets (Vitaflo International Ltd)

30 sachet (ACBS) . NHS indicative price = £122.64

Homocystinuria or hypermethioninaemia

HCU Anamix ® Infant

▶ Nutritional supplement for the dietary management of proven

vitamin B6 non-responsive homocystinuria or

hypermethioninaemia in children from birth to 3 years.

POWDER, protein equivalent (essential and non-essential amino

acids except methionine) 13.1 g, carbohydrate 49.5 g, fat 23 g,

fibre 5.3 g, energy 1915 kJ (457 kcal)/100 g, with vitamins,

minerals, and trace elements; standard dilution (15%) provides

protein equivalent 2 g, carbohydrate 7.4 g, fat 3.5 g, fibre

800 mg, energy 287 kJ (69 kcal)/100 mL.

HCU Anamix Infant powder (Nutricia Ltd)

400 gram (ACBS) . NHS indicative price = £42.17

BNF 78 Nutritional supplements for metabolic diseases 1581

Borderline substances | Appendix 2

A2

HCU cooler ® 15

▶ A methionine-free protein substitute for use as a nutritional

supplement in children over 3 years with homocystinuria.

LIQUID, protein (essential and non-essential amino acids except

methionine) 15 g, carbohydrate 7 g, fat 500 mg, energy 393 kJ

(92 kcal)/130 mL, with vitamins, minerals, and trace elements.

HCU orange cooler 15 liquid (Vitaflo International Ltd)

130 ml (ACBS) . NHS indicative price = £12.31

HCU Express ® 15

▶ A methionine-free protein substitute for use as a nutritional

supplement in children over 8 years with homocystinuria.

POWDER, protein (essential and non-essential amino acids

except methionine) 15 g, carbohydrate 3.8 g, fat 30 mg, energy

315 kJ (75.3 kcal)/25 g with vitamins, minerals, and trace

elements. To flavour unflavoured products, see FlavourPac

p. 1575.

HCU express 15 oral powder 25g sachets (Vitaflo International Ltd)

30 sachet (ACBS) . NHS indicative price = £362.37

HCU Express ® 20

▶ A methionine-free protein substitute for use as a nutritional

supplement in children over 8 years with homocystinuria.

POWDER, protein (essential and non-essential amino acids

except methionine) 20 g, carbohydrate 4.7 g, fat 70 mg, energy

416 kJ (99 kcal)/34 g with vitamins, minerals, and trace

elements. To flavour unflavoured products, see FlavourPac

p. 1575

HCU express 20 oral powder 34g sachets (Vitaflo International Ltd)

30 sachet (ACBS) . NHS indicative price = £468.17

HCU gel ®

▶ A methionine-free protein substitute for use as a nutritional

supplement for the dietary management of children 1–10 years

with homocystinuria.

POWDER, protein (essential and non-essential amino acids

except methionine) 10 g, carbohydrate 10.3 g, fat 20 mg, energy

339 kJ (81 kcal)/24 g with vitamins, minerals, and trace

elements. To flavour unflavoured products, see FlavourPac

p. 1575.

HCU gel oral powder 24g sachets (Vitaflo International Ltd)

30 sachet (ACBS) . NHS indicative price = £233.29

HCU Lophlex ® LQ 20

▶ Nutritional supplement for the dietary management of

homocystinuria in children over 3 years.

LIQUID, protein equivalent (essential and non-essential amino

acids except methionine) 20 g, carbohydrate 8.8 g, fat 440 mg,

energy 509 kJ (120 kcal)/125 mL, with vitamins, minerals, and

trace elements.

HCU Lophlex LQ 20 liquid (Nutricia Ltd)

125 ml (ACBS) . NHS indicative price = £17.39

HCU LV ®

▶ Nutritional supplement for the dietary management of

hypermethioninaemia or vitamin B6 non-responsive

homocystinuria in children over 8 years.

POWDER, protein (essential and non-essential amino acids

except methionine) 20 g, carbohydrate 2.5 g, fat 190 mg, energy

390 kJ (92 kcal)/27.8-g sachet, with vitamins, minerals, and

trace elements. To flavour unflavoured products, see Modjul

Flavour System p. 1576.

HCU-LV oral powder 27.8g sachets tropical (Nutricia Ltd)

30 sachet (ACBS) . NHS indicative price = £534.80

HCU-LV oral powder 27.8g sachets unflavoured (Nutricia Ltd)

30 sachet (ACBS) . NHS indicative price = £534.80

XMET Homidon ®

▶ Nutritional supplement for the dietary management of

hypermethioninaemia or homocystinuria in children and

adults.

POWDER, protein equivalent (essential and non-essential amino

acids, except methionine) 77 g, carbohydrate 4.5 g, fat nil,

energy 1386 kJ (326 kcal)/100 g. To flavour unflavoured

products, see Modjul Flavour System p. 1576.

XMET Homidon powder (Nutricia Ltd)

500 gram (ACBS) . NHS indicative price = £201.74

HCU Maxamum ®

▶ Nutritional supplement for the dietary management of

hypermethioninaemia or homocystinuria.

POWDER, protein equivalent (essential and non-essential amino

acids except methionine) 39 g, carbohydrate 34 g, fat less than

500 mg, energy 1260 kJ (297 kcal)/100 g, with vitamins,

minerals, and trace elements. To flavour unflavoured products,

see Modjul Flavour System p. 1576. Maxamum products are

generally intended for use in children over 8 years.

HCU Maxamum powder (Nutricia Ltd)

500 gram (ACBS) . NHS indicative price = £170.70

Hyperlysinaemia

▶ Nutritional supplement for the dietary management of proven

hyperlysinaemia in children from birth to 3 years.

HYPER LYS Anamix ® Infant

▶ Nutritional supplement for the dietary management of proven

hyperlysinaemia in children from birth to 3 years.

POWDER, protein equivalent (essential and non-essential amino

acids except lysine) 13.1 g, carbohydrate 49.5 g, fat 23 g, fibre

5.3 g, energy 1915 kJ (457 kcal)/100 g, with vitamins, minerals,

and trace elements; standard dilution (15%) provides protein

equivalent 2 g, carbohydrate 7.4 g, fat 3.5 g, fibre 800 mg, energy

287 kJ (69 kcal)/100 mL.

HYPER LYS Anamix Infant powder (Nutricia Ltd)

400 gram (ACBS) . NHS indicative price = £42.17

Isovaleric acidaemia

▶ Nutritional supplement for the dietary management of proven

isovaleric acidaemia or other proven disorders of leucine

metabolism in children from birth to 3 years.

IVA Anamix ® Infant

▶ Nutritional supplement for the dietary management of proven

isovaleric acidaemia or other proven disorders of leucine

metabolism in children from birth to 3 years.

POWDER, protein equivalent (essential and non-essential amino

acids except leucine) 13.1 g, carbohydrate 49.5 g, fat 23 g, fibre

5.3 g, energy 1915 kJ (457 kcal)/100 g, with vitamins, minerals,

and trace elements; standard dilution (15%) provides protein

equivalent 2 g, carbohydrate 7.4 g, fat 3.5 g, fibre 800 mg, energy

287 kJ (69 kcal)/100 mL.

IVA Anamix Infant powder (Nutricia Ltd)

400 gram (ACBS) . NHS indicative price = £42.17

Maple syrup urine disease

MSUD Aid III ®

▶ Nutritional supplement for the dietary management of maple

syrup urine disease and related conditions in children and

adults where it is necessary to limit the intake of branched

chain amino acids.

POWDER, protein equivalent (essential and non-essential amino

acids except isoleucine, leucine, and valine) 77 g, carbohydrate

4.5 g, fat nil, energy 1386 kJ (326 kcal)/100 g. To flavour

unflavoured products, see Modjul Flavour System p. 1576.

MSUD Aid 111 powder (Nutricia Ltd)

500 gram (ACBS) . NHS indicative price = £201.74

MSUD Anamix ® Infant

▶ Nutritional supplement for the dietary management of proven

maple syrup urine disease in children from birth to 3 years.

POWDER, protein equivalent (essential and non-essential amino

acids except isoleucine, leucine, and valine) 13.1 g,

carbohydrate 49.5 g, fat 23 g, fibre 5.3 g, energy 1915 kJ

(457 kcal)/100 g, with vitamins, minerals, and trace elements;

standard dilution (15%) provides protein equivalent 2 g,

carbohydrate 7.4 g, fat 3.5 g, fibre 800 mg, energy 287 kJ

(69 kcal)/100 mL.

MSUD Anamix Infant powder (Nutricia Ltd)

400 gram (ACBS) . NHS indicative price = £42.17

1582 Nutritional supplements for metabolic diseases BNF 78

Borderline substances | Appendix 2

A2

MSUD Anamix ® Junior LQ

▶ Nutritional supplement for the dietary management of maple

syrup urine disease in children 1–10 years.

LIQUID, protein equivalent (essential and non-essential amino

acids except isoleucine, leucine, and valine) 10 g, carbohydrate

8.8 g, fat 4.8 g, fibre 310 mg, energy 497 kJ (118 kcal)/125 mL,

with vitamins, minerals, and trace elements. Lactose-free.

MSUD Anamix Junior LQ liquid (Nutricia Ltd)

125 ml (ACBS) . NHS indicative price = £9.78

MSUD cooler ® 15

▶ Nutritional supplement for the dietary management of maple

syrup urine disease in children over 3 years and adults.

LIQUID, protein equivalent (essential and non-essential amino

acids except leucine, isoleucine, and valine) 15 g, carbohydrate

7 g, fat 500 mg, energy 393 kJ (92 kcal)/130-mL pouch, with

vitamins, minerals, and trace elements.

MSUD orange cooler 15 liquid (Vitaflo International Ltd)

130 ml (ACBS) . NHS indicative price = £12.31

MSUD red cooler 15 liquid (Vitaflo International Ltd)

130 ml (ACBS) . NHS indicative price = £12.31

MSUD express ® 15

▶ Nutritional supplement for the dietary management of maple

syrup urine disease in children over 8 years and adults.

POWDER, protein equivalent (essential and non-essential amino

acids except leucine, isoleucine, and valine) 15 g, carbohydrate

3.8 g, fat less than 100 mg, energy 315 kJ (75 kcal)/25 g, with

vitamins, minerals, and trace elements. To flavour unflavoured

products, see FlavourPac p. 1575.

MSUD express 15 oral powder 25g sachets (Vitaflo International Ltd)

30 sachet (ACBS) . NHS indicative price = £362.37

MSUD express ® 20

▶ Nutritional supplement for the dietary management of maple

syrup urine disease in children over 8 years and adults.

POWDER, protein equivalent (essential and non-essential amino

acids except leucine, isoleucine, and valine) 20 g, carbohydrate

4.7 g, fat less than 100 mg, energy 416 kJ (99 kcal)/34 g, with

vitamins, minerals, and trace elements. To flavour unflavoured

products, see FlavourPac p. 1575.

MSUD express 20 oral powder 34g sachets (Vitaflo International Ltd)

30 sachet (ACBS) . NHS indicative price = £468.17

MSUD Gel ®

▶ Nutritional supplement for the dietary management of maple

syrup urine disease in children 1–10 years.

POWDER, protein equivalent (essential and non-essential amino

acids except leucine, isoleucine, and valine) 10 g, carbohydrate

10.3 g, fat less than 100 mg, energy 339 kJ (81 kcal)/24 g, with

vitamins, minerals, and trace elements. To flavour unflavoured

products, see FlavourPac p. 1575.

MSUD gel 24g sachets (Vitaflo International Ltd)

30 sachet (ACBS) . NHS indicative price = £236.03

MSUD Lophlex ® LQ 20

▶ Nutritional supplement for the dietary management of maple

syrup urine disease in children over 3 years.

LIQUID, protein equivalent (essential and non-essential amino

acids except isoleucine, leucine, and valine) 20 g, carbohydrate

8.8 g, fat less than 500 mg, energy 509 kJ (120 kcal)/125 mL, with

vitamins, minerals, and trace elements.

MSUD Lophlex LQ 20 liquid (Nutricia Ltd)

125 ml (ACBS) . NHS indicative price = £17.39

MSUD Maxamum ®

▶ Nutritional supplement for the dietary management of maple

syrup urine disease.

POWDER, protein equivalent (essential and non-essential amino

acids except isoleucine, leucine, and valine) 39 g, carbohydrate

34 g, fat less than 500 mg, energy 1260 kJ (297 kcal)/100 g, with

vitamins, minerals, and trace elements. To flavour unflavoured

products, see Modjul Flavour System p. 1576.

Maxamum products are generally intended for use in children

over 8 years.

MSUD Maxamum powder orange (Nutricia Ltd)

500 gram (ACBS) . NHS indicative price = £170.70

MSUD Maxamum powder unflavoured (Nutricia Ltd)

500 gram (ACBS) . NHS indicative price = £170.70

Methylmalonic or propionic acidaemia

MMA/PA Anamix ® Infant

▶ Nutritional supplement for the dietary management of proven

methylmalonic acidaemia or propionic acidaemia in children

from birth to 3 years.

POWDER, protein equivalent (essential and non-essential amino

acids except methionine, threonine, and valine, and low

isoleucine) 13.1 g, carbohydrate 49.5 g, fat 23 g, fibre 5.3 g,

energy 1915 kJ (457 kcal)/100 g, with vitamins, minerals, and

trace elements; standard dilution (15%) provides protein

equivalent 2 g, carbohydrate 7.4 g, fat 3.5 g, fibre 800 mg, energy

287 kJ (69 kcal)/100 mL.

MMA / PA Anamix Infant powder (Nutricia Ltd)

400 gram (ACBS) . NHS indicative price = £42.17

XMTVI Asadon ®

▶ Nutritional supplement for the dietary management of

methylmalonic acidaemia or propionic acidaemia in children

and adults.

POWDER, protein equivalent (essential and non-essential amino

acids except methionine, threonine, and valine, and low

isoleucine) 77 g, carbohydrate 4.5 g, fat nil, energy 1386 kJ

(326 kcal)/100 g. To flavour unflavoured products, see Modjul

Flavour System p. 1576.

XMTVI Asadon powder (Nutricia Ltd)

200 gram (ACBS) . NHS indicative price = £80.69

MMA/PA Maxamum ®

▶ Nutritional supplement for the dietary management of

methylmalonic acidaemia or propionic acidaemia.

POWDER, protein equivalent (essential and non-essential amino

acids except methionine, threonine, and valine, and low

isoleucine) 39 g, carbohydrate 34 g, fat less than 500 mg, energy

1260 kJ (297 kcal)/100 g, with vitamins, minerals, and trace

elements. To flavour unflavoured products, see Modjul Flavour

System p. 1576.

Maxamum products are generally intended for use in

children over 8 years.

MMA/PA Maxamum powder (Nutricia Ltd)

500 gram (ACBS) . NHS indicative price = £170.70

Other inborn errors of metabolism

Cystine500 ®

▶ Nutritional supplement for the dietary management of inborn

errors of amino acid metabolism in adults and children from

3 years.

POWDER, cystine 500 mg, carbohydrate 3.3 g, fat nil, energy

64 kJ (15 kcal)/4 g

Cystine500 oral powder sachets (Vitaflo International Ltd)

30 sachet (ACBS) . NHS indicative price = £59.28

DocOmega ®

▶ Nutritional supplement for the dietary management of inborn

errors of metabolism for adults and children from birth.

POWDER, protein (cows’ milk, soya) 100 mg, carbohydrate 3.2 g,

fat 500 mg (of which docosahexaenoic acid 200 mg), fibre nil,

energy 74 kJ (18 kcal)/4 g, with minerals

DocOmega oral powder 4g sachets (Vitaflo International Ltd)

30 sachet (ACBS) . NHS indicative price = £42.90

EAA ® Supplement

▶ Nutritional supplement for the dietary management of

disorders of protein metabolism including urea cycle disorders

in children over 3 years.

POWDER, protein equivalent (essential amino acids) 5 g,

carbohydrate 4 g, fat nil, energy 151 kJ (36 kcal)/12.5 g, with

vitamins, minerals, and trace elements.

EAA Supplement oral powder 12.5g sachets (Vitaflo International Ltd)

50 sachet (ACBS) . NHS indicative price = £223.68

BNF 78 Nutritional supplements for metabolic diseases 1583

Borderline substances | Appendix 2

A2

Isoleucine50 ®

▶ Nutritional supplement for use in the dietary management of

inborn errors of amino acid metabolism in adults and children

from birth.

POWDER, isoleucine 50 mg, carbohydrate 3.8 g, fat nil, energy

63 kJ (15 kcal)/4 g

Isoleucine50 oral powder 4g sachets (Vitaflo International Ltd)

30 sachet (ACBS) . NHS indicative price = £59.28

KeyOmega ®

▶ Nutritional supplement for the dietary management of inborn

errors of metabolism.

POWDER, protein (cows’ milk, soya) 170 mg, carbohydrate 2.8 g,

fat 800 mg (of which arachidonic acid 200 mg, docosahexaenoic

acid 100 mg), energy 80 kJ (19 kcal)/4 g.

KeyOmega oral powder 4g sachets (Vitaflo International Ltd)

30 sachet (ACBS) . NHS indicative price = £43.87

Leucine100 ®

▶ Nutritional supplement for the dietary management of inborn

errors of amino acid metabolism in adults and children from

birth.

POWDER, leucine 100 mg, carbohydrate 3.7 g, fat nil, energy

63 kJ (15 kcal)/4 g

Leucine100 oral powder sachets (Vitaflo International Ltd)

30 sachet (ACBS) . NHS indicative price = £59.28

Low protein drink

▶ Nutritional supplement for the dietary management of inborn

errors of amino acid metabolism in adults and children over

1 year.

POWDER, protein (cows’ milk) 4.5 g (phenylalanine 100 mg),

carbohydrate 59.5 g, fat 29.9 g, fibre nil, energy 2194 kJ

(528 kcal)/100 g, with vitamins, minerals, and trace elements.

Contains lactose.

Termed Milupa ® lp-drink by manufacturer.

Milupa LP drink (Nutricia Ltd)

400 gram (ACBS) . NHS indicative price = £10.00

Phenylalanine50 ®

▶ Nutritional supplement for use in the dietary management of

inborn errors of metabolism in adults and children from birth.

POWDER, phenylalanine 50 mg, carbohydrate 3.8 g, fat nil,

energy 63 kJ (15 kcal)/4 g

Phenylalanine50 oral powder sachets (Vitaflo International Ltd)

30 sachet (ACBS) . NHS indicative price = £57.56

ProZero ®

▶ A protein-free nutritional supplement for the dietary

management of inborn errors of metabolism in children over

6 months and adults.

LIQUID, carbohydrate 8.1 g (of which sugars 3.5 g), fat 3.8 g,

energy 278 kJ (66 kcal)/100 mL. Contains lactose.

ProZero liquid (Vitaflo International Ltd)

250 ml (ACBS) . NHS indicative price = £1.58 | 1000 ml (ACBS) . NHS indicative price = £6.31

Tyrosine1000 ®

▶ Nutritional supplement for the dietary management of inborn

errors of amino acid metabolism in adults and children from

birth.

POWDER, tyrosine 1 g, carbohydrate 2.9 g, fat nil, energy 63 kJ

(15 kcal)/4-g sachet.

Tyrosine1000 oral powder 4g sachets (Vitaflo International Ltd)

30 sachet (ACBS) . NHS indicative price = £5.42

Valine50 ®

▶ Nutritional supplement for the dietary management of inborn

errors of amino acid metabolism in adults and children from

birth.

POWDER, valine 50 mg, carbohydrate 3.8 g, fat nil, energy 63 kJ

(15 kcal)/4 g

Valine50 oral powder 4g sachets (Vitaflo International Ltd)

30 sachet (ACBS) . NHS indicative price = £59.28

Phenylketonuria

Easiphen ®

▶ Nutritional supplement for the dietary management of proven

phenylketonuria in children over 8 years.

LIQUID, protein equivalent (containing essential and nonessential amino acids except phenylalanine) 6.7 g, carbohydrate

5.1 g, fat 2 g, energy 275 kJ (65 kcal)/100 mL with vitamins,

minerals, and trace elements.

Easiphen liquid (Nutricia Ltd)

250 ml (ACBS) . NHS indicative price = £10.46

L-Tyrosine

▶ Nutritional supplement for the dietary management of

phenylketonuria in pregnant women with low plasma tyrosine

concentrations.

POWDER, L-tyrosine 20 g, carbohydrate 76.8 g, fat nil, energy

1612 kJ (379 kcal)/100 g.

L-Tyrosine powder (Nutricia Ltd)

100 gram (ACBS) . NHS indicative price = £23.76

Lophlex ®

▶ Nutritional supplement for the dietary management of proven

phenylketonuria in children over 8 years and adults including

pregnant women.

POWDER, protein equivalent (essential and non-essential amino

acids except phenylalanine) 20 g, carbohydrate 2.5 g, fat 60 mg,

fibre 220 mg, energy 385 kJ (91 kcal)/27.8-g sachet, with

vitamins, minerals, and trace elements.

Lophlex powder 27.8g sachets berry (Nutricia Ltd)

30 sachet (ACBS) . NHS indicative price = £314.10

Lophlex powder 27.8g sachets orange (Nutricia Ltd)

30 sachet (ACBS) . NHS indicative price = £314.10

Lophlex powder 27.8g sachets unflavoured (Nutricia Ltd)

30 sachet (ACBS) . NHS indicative price = £314.10

Loprofin ® PKU Drink

▶ Nutritional supplement for the dietary management of

phenylketonuria in children over 1 year and adults.

LIQUID, protein (cows’ milk) 400 mg (phenylalanine 10 mg),

lactose 9.4 g, fat 2 g, energy 165 kJ (40 kcal)/100 mL.

Loprofin PKU drink (Nutricia Ltd)

200 ml (ACBS) . NHS indicative price = £0.81

Loprofin ® Sno-Pro

▶ Nutritional supplement for the dietary management of

phenylketonuria, chronic renal failure and other inborn errors

of amino acid metabolism.

LIQUID, protein (cows’ milk) 220 mg (phenylalanine 12.5 mg),

carbohydrate 8 g, fat 3.8 g, energy 273 kJ (65 kcal)/100 mL.

Contains lactose.

Loprofin SNO-PRO drink (Nutricia Ltd)

200 ml (ACBS) . NHS indicative price = £1.35

Phlexy-10 ® Exchange System

▶ Nutritional supplement for the dietary management of

phenylketonuria.

CAPSULES, protein equivalent (essential and non-essential

amino acids except phenylalanine) 416.5 mg/capsule.

Phlexy-10 500mg capsules (Nutricia Ltd)

200 capsule (ACBS) . NHS indicative price = £47.03

TABLETS, protein equivalent (essential and non-essential amino

acids except phenylalanine) 833 mg tablet.

Phlexy-10 tablets (Nutricia Ltd)

75 tablet (ACBS) . NHS indicative price = £30.24

DRINK MIX, powder, protein equivalent (essential and nonessential amino acids except phenylalanine) 8.33 g,

carbohydrate 8.8 g/20-g sachet.

Phlexy-10 drink mix 20g sachets apple & blackcurrant (Nutricia

Ltd)

30 sachet (ACBS) . NHS indicative price = £139.28

Phlexy-10 drink mix 20g sachets citrus burst (Nutricia Ltd)

30 sachet (ACBS) . NHS indicative price = £139.28

Phlexy-10 drink mix 20g sachets tropical surprise (Nutricia Ltd)

30 sachet (ACBS) . NHS indicative price = £139.28

1584 Nutritional supplements for metabolic diseases BNF 78

Borderline substances | Appendix 2

A2

Phlexy-Vits ®

▶ For use as a vitamin and mineral component of restricted

therapeutic diets in children over 11 years and adults with

phenylketonuria and similar amino acid abnormalities.

POWDER, vitamins, minerals, and trace elements

Phlexy-Vits powder 7g sachets (Nutricia Ltd)

30 sachet (ACBS) . NHS indicative price = £77.23

TABLETS, vitamins, minerals, and trace elements

Phlexy-Vits tablets (Nutricia Ltd)

180 tablet (ACBS) . NHS indicative price = £88.51

PK Aid 4 ®

▶ Nutritional supplement for the dietary management of

phenylketonuria in children and adults.

POWDER, protein equivalent (essential and non-essential amino

acids except phenylalanine) 79 g, carbohydrate 4.5 g, fat nil,

energy 1420 kJ (334 kcal)/100 g. To flavour unflavoured

products, see Modjul Flavour System p. 1576

PK Aid 4 powder (Nutricia Ltd)

500 gram (ACBS) . NHS indicative price = £155.07

PKU Anamix ® Infant

▶ Nutritional supplement for the dietary management of proven

phenylketonuria in children from birth to 3 years.

POWDER, protein equivalent (essential and non-essential amino

acids except phenylalanine) 13.1 g, carbohydrate 49.5 g, fat 23 g,

fibre 5.3 g, energy 1915 kJ (457 kcal)/100 g, with vitamins,

minerals, and trace elements; standard dilution (15%) provides

protein equivalent 2 g, carbohydrate 7.4 g, fat 3.5 g, fibre

800 mg, energy 287 kJ (69 kcal)/100 mL

PKU Anamix Infant powder (Nutricia Ltd)

400 gram (ACBS) . NHS indicative price = £37.08

PKU Anamix ® Junior

▶ Nutritional supplement for the dietary management of

phenylketonuria in children 1–10 years.

POWDER, protein equivalent (essential and non-essential amino

acids except phenylalanine) 10 g, carbohydrate 11.5 g, fat 4.5 g,

energy 566 kJ (135 kcal)/36-g sachet, with vitamins, minerals,

and trace elements

PKU Anamix Junior powder 36g sachets chocolate (Nutricia Ltd)

30 sachet (ACBS) . NHS indicative price = £137.10

PKU Anamix Junior powder 36g sachets neutral (Nutricia Ltd)

30 sachet (ACBS) . NHS indicative price = £137.10

PKU Anamix Junior powder 36g sachets berry (Nutricia Ltd)

30 sachet (ACBS) . NHS indicative price = £137.10

PKU Anamix Junior powder 36g sachets orange (Nutricia Ltd)

30 sachet (ACBS) . NHS indicative price = £137.10

PKU Anamix ® Junior LQ

▶ Nutritional supplement for the dietary supplement of

phenyketonuria in children 1–10 years.

LIQUID, protein equivalent (essential and non-essential amino

acids except phenylalanine) 10 g, carbohydrate 8.8 g, fat 4.8 g,

fibre 310 mg, energy 497 kJ (118 kcal)/125 mL, with vitamins,

minerals, and trace elements. Lactose-free.

PKU Anamix Junior LQ liquid berry (Nutricia Ltd)

125 ml (ACBS) . NHS indicative price = £6.08

PKU Anamix Junior LQ liquid orange (Nutricia Ltd)

125 ml (ACBS) . NHS indicative price = £6.08

PKU cooler10 ®

▶ Nutritional supplement for the dietary management of

phenylketonuria in children over 3 years.

LIQUID, protein equivalent (essential and non-essential amino

acids except phenylalanine) 10 g, carbohydrate 4.7 g, energy

258 kJ (62 kcal)/87-mL pouch, with vitamins, minerals, and trace

elements.

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